Electrocardiographic findings in Rett syndrome

An explanation for sudden death?

Elizabeth Sekul, Jeffrey P. Moak, Rebecca J. Schultz, Daniel G. Glaze, J. Kay Dunn, Alan K. Percy

Research output: Contribution to journalArticle

92 Citations (Scopus)

Abstract

Girls with Rett syndrome had significantly longer corrected QT intervals (p <0.001) and more T-wave abnormalities (p <0.001) than were found in age-matched healthy girls. With advancing stages of the syndrome, the proportion of corrected QT interval prolongations and T-wave changes increased. The findings suggest a possible cardiac basis for sudden, unexpected death in Rett syndrome. (J PEDIATR 1994;125:80-2)

Original languageEnglish (US)
Pages (from-to)80-82
Number of pages3
JournalJournal of Pediatrics
Volume125
Issue number1
DOIs
StatePublished - Jan 1 1994
Externally publishedYes

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Rett Syndrome
Sudden Death

Keywords

  • Corrected QT interval
  • QTc
  • RS
  • Rett-syndrome

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

Cite this

Electrocardiographic findings in Rett syndrome : An explanation for sudden death? / Sekul, Elizabeth; Moak, Jeffrey P.; Schultz, Rebecca J.; Glaze, Daniel G.; Dunn, J. Kay; Percy, Alan K.

In: Journal of Pediatrics, Vol. 125, No. 1, 01.01.1994, p. 80-82.

Research output: Contribution to journalArticle

Sekul, Elizabeth ; Moak, Jeffrey P. ; Schultz, Rebecca J. ; Glaze, Daniel G. ; Dunn, J. Kay ; Percy, Alan K. / Electrocardiographic findings in Rett syndrome : An explanation for sudden death?. In: Journal of Pediatrics. 1994 ; Vol. 125, No. 1. pp. 80-82.
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