Electrocardiographic findings in Rett syndrome: An explanation for sudden death?

Elizabeth A. Sekul, Jeffrey P. Moak, Rebecca J. Schultz, Daniel G. Glaze, J. Kay Dunn, Alan K. Percy

Research output: Contribution to journalArticle

96 Scopus citations

Abstract

Girls with Rett syndrome had significantly longer corrected QT intervals (p <0.001) and more T-wave abnormalities (p <0.001) than were found in age-matched healthy girls. With advancing stages of the syndrome, the proportion of corrected QT interval prolongations and T-wave changes increased. The findings suggest a possible cardiac basis for sudden, unexpected death in Rett syndrome. (J PEDIATR 1994;125:80-2)

Original languageEnglish (US)
Pages (from-to)80-82
Number of pages3
JournalJournal of Pediatrics
Volume125
Issue number1
DOIs
Publication statusPublished - Jan 1 1994
Externally publishedYes

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Keywords

  • Corrected QT interval
  • QTc
  • RS
  • Rett-syndrome

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

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