Hallervorden‐spatz syndrome: Clinical and magnetic resonance imaging correlations

K. D. Sethi, R. J. Adams, D. W. Loring, T. El Gammal

Research output: Contribution to journalArticlepeer-review

173 Scopus citations


Two women with a presumptive diagnosis of Hallervor‐den‐Spatz syndrome had a combination of dystonia and parkinsonism. One had retinitis pigmentosa. Neuropsychological testing revealed Decemberreased verbal fluency and visuoconstructional and motor deficits. Magnetic resonance imaging performed with a high‐field‐strength unit (1.5 Tesla) showed striking abnormalities in the globus pallidus bilaterally (“eye‐of‐the‐tiger” sign). Magnetic resonance imaging may prove useful in the diagnosis of Hallervorden‐Spatz syndrome.

Original languageEnglish (US)
Pages (from-to)692-694
Number of pages3
JournalAnnals of Neurology
Issue number5
StatePublished - Nov 1988

ASJC Scopus subject areas

  • Neurology
  • Clinical Neurology


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