Hallervorden‐spatz syndrome: Clinical and magnetic resonance imaging correlations

Kapil Dev Sethi, R. J. Adams, D. W. Loring, T. El Gammal

Research output: Contribution to journalArticle

166 Citations (Scopus)

Abstract

Two women with a presumptive diagnosis of Hallervor‐den‐Spatz syndrome had a combination of dystonia and parkinsonism. One had retinitis pigmentosa. Neuropsychological testing revealed Decemberreased verbal fluency and visuoconstructional and motor deficits. Magnetic resonance imaging performed with a high‐field‐strength unit (1.5 Tesla) showed striking abnormalities in the globus pallidus bilaterally (“eye‐of‐the‐tiger” sign). Magnetic resonance imaging may prove useful in the diagnosis of Hallervorden‐Spatz syndrome.

Original languageEnglish (US)
Pages (from-to)692-694
Number of pages3
JournalAnnals of Neurology
Volume24
Issue number5
DOIs
StatePublished - Jan 1 1988

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Magnetic Resonance Imaging
Globus Pallidus
Retinitis Pigmentosa
Dystonia
Parkinsonian Disorders

ASJC Scopus subject areas

  • Neurology
  • Clinical Neurology

Cite this

Hallervorden‐spatz syndrome : Clinical and magnetic resonance imaging correlations. / Sethi, Kapil Dev; Adams, R. J.; Loring, D. W.; El Gammal, T.

In: Annals of Neurology, Vol. 24, No. 5, 01.01.1988, p. 692-694.

Research output: Contribution to journalArticle

Sethi, Kapil Dev ; Adams, R. J. ; Loring, D. W. ; El Gammal, T. / Hallervorden‐spatz syndrome : Clinical and magnetic resonance imaging correlations. In: Annals of Neurology. 1988 ; Vol. 24, No. 5. pp. 692-694.
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