Pentalogy of Cantrell associated with hypoplastic left heart syndrome

D. S. Wheeler, J. D. St. Louis

Research output: Contribution to journalArticlepeer-review

14 Scopus citations


Pentalogy of Cantrell is a rare anomaly characterized by midline closure defects, including a defect in the lower sternum, supraumbilical abdominal wall defect, deficiency of the anterior portion of the diaphragm, deficiency in the diaphragmatic portion of the pericardium with free communication between the pericardial and peritoneal cavities, and congenital heart defects. The long-term prognosis for children with this anomaly depends to a great extent on the complexity of the associated congenital heart defect. We describe the previously unreported association of pentalogy of Cantrell with hypoplastic left heart syndrome.

Original languageEnglish (US)
Pages (from-to)311-313
Number of pages3
JournalPediatric Cardiology
Issue number4
StatePublished - Aug 2007


  • Hypoplastic left heart syndrome
  • Omphalocele
  • Pentalogy of Cantrell
  • Single ventricle

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine


Dive into the research topics of 'Pentalogy of Cantrell associated with hypoplastic left heart syndrome'. Together they form a unique fingerprint.

Cite this