TY - JOUR
T1 - Posterior occipitoatlantal hypermobility in down syndrome
T2 - An analysis of 199 patients
AU - Parfenchuck, Thomas A.
AU - Bertrand, Styles L
AU - Powers, Mark J.
AU - Drvaric, David M.
AU - Pueschel, Siegfried M.
AU - Roberts, John M.
PY - 1994
Y1 - 1994
N2 - We endeavored to determine the prevalence of occipitoatlantal hypermobility in individuals with Down syndrome, to establish objective radiographic criteria for this entity, and to correlate this with neurologic abnormality. In a retrospective analysis, upper cervical spine radiographs of 210 patients with Down syndrome were compared with those of 102 normal individuals. Radiographs were evaluated using the Powers ratio. Patients identified with radiographic evidence of posterior occipitoatlantal hypermobility were then examined clinically and compared with a matched group of patients with Down syndrome and normal Powers ratios. Of the patients with Down syndrome, 8.5% had a Powers ratio of <0.55, which was indicative of posterior occipitoatlantal hypermobility (POAH). Furthermore, 66% of those with an abnormal Powers ratio had positive neurologic findings upon physical exam, a finding that was statistically significant when compared to a matched group of patients with Down syndrome and normal Powers ratio.
AB - We endeavored to determine the prevalence of occipitoatlantal hypermobility in individuals with Down syndrome, to establish objective radiographic criteria for this entity, and to correlate this with neurologic abnormality. In a retrospective analysis, upper cervical spine radiographs of 210 patients with Down syndrome were compared with those of 102 normal individuals. Radiographs were evaluated using the Powers ratio. Patients identified with radiographic evidence of posterior occipitoatlantal hypermobility were then examined clinically and compared with a matched group of patients with Down syndrome and normal Powers ratios. Of the patients with Down syndrome, 8.5% had a Powers ratio of <0.55, which was indicative of posterior occipitoatlantal hypermobility (POAH). Furthermore, 66% of those with an abnormal Powers ratio had positive neurologic findings upon physical exam, a finding that was statistically significant when compared to a matched group of patients with Down syndrome and normal Powers ratio.
KW - Craniocervical region
KW - Down syndrome
KW - Occipitoatlantal hypermobility
KW - Powers ratio
KW - Radiographic sign
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U2 - 10.1097/01241398-199405000-00006
DO - 10.1097/01241398-199405000-00006
M3 - Article
C2 - 8006159
AN - SCOPUS:0028227051
SN - 0271-6798
VL - 14
SP - 304
EP - 308
JO - Journal of Pediatric Orthopaedics
JF - Journal of Pediatric Orthopaedics
IS - 3
ER -